Atypical Psychiatric Features in Sporadic Creutzfeldt-Jacob Disease: A Diagnostic Challenge
نویسنده
چکیده
Creutzfeldt-Jacob disease is a rare and fatal prion disease comprised of four variants: familial, sporadic, variant, and iatrogenic. Classic presenting symptoms include a rapidly progressive dementia, myoclonus, and ataxia. Misdiagnosis often occurs due to the neuropsychiatric phenotypic variability of CJD. Psychiatric manifestations across all four types of CJD are now increasingly being recognized, leading to earlier detection. We present a case of sporadic Creutzfeldt-Jacob disease with atypical psychiatric features and sparing of motor symptoms six months after initial clinical presentation.
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